2024年1月16日 · Scimitar syndrome, also known as hypogenetic lung syndrome, is characterized by a hypoplastic lung that is drained by an anomalous pulmonary vein into the systemic venous system. It is a type of partial anomalous pulmonary venous return and is one of the several findings in congenital pulmonary venolobar syndrome .

Scimitar syndrome, or congenital pulmonary venolobar syndrome, is a rare congenital heart defect characterized by anomalous venous return from the right lung (to the systemic venous drainage, rather than directly to the left atrium). [1]

2022年4月11日 · In scimitar syndrome, one or more of your pulmonary veins carries blood into the right side of your heart instead of the left side. Sometimes, your right lung may also receive blood from your aorta instead of your pulmonary arteries.

2023年6月26日 · Scimitar syndrome is primarily an imaging diagnosis and gives a characteristic abnormal chest X-ray that shows the shadow of the descending pulmonary vein along the right cardiac border, a hypoplastic lung, as well as dextroposition of the heart.

2010年6月15日 · Scimitar, or pulmonary venolobar, syndrome is a rare but well-known congenital cardiovascular defect that includes a hypoplastic right pulmonary artery and right lung, which leads to displacement of cardiac structures into the right hemithorax, anomalous systemic arterial supply to the right lung, and a characteristically curved anomalous right ...

Regardless of whether the long baffle technique or division and reimplantation of the scimitar vein into an atrium is used, pulmonary venous stenosis, obstruction, and thrombosis remain the major obstacles to a successful repair in scimitar syndrome.

2020年11月3日 · The scimitar syndrome is a complex malformation of the heart, lungs, and blood vessels. The main feature of this malformation is the anomalous drainage of the pulmonary veins into the inferior vena cava.

Scimitar syndrome describes a specific subset of partial anomalous pulmonary venous return (PAPVR) in which an anomalous right sided pulmonary vein(s) drains either above or below the diaphragm into the inferior vena cava.

Scimitar syndrome is a rare congenital anomaly in which there is an anomalous pulmonary vein drain- ing most or all of the right lung into the inferior vena cava near the entrance to the atrium. The name is derived from the curved appearance of the anomalous vein on chest X-ray, which resembles a “Turkish sword” or scimitar.

Scimitar syndrome is a rare association of congenital cardiopulmonary anomalies characterized by partial anomalous pulmonary venous return, in which an abnormal right pulmonary vein drains into the inferior vena cava.